AN UNUSUAL MANIFESTATION OF CARDIAC AMYLOIDOSIS ON ELECTROCARDIOGRAM
Journal Name:
- İstanbul Tıp Fakültesi Dergisi
Key Words:
Keywords (Original Language):
Author Name | University of Author | Faculty of Author |
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Abstract (2. Language):
The most common clinical presentation of amyloid light chain amyloidosis (AL-A) includes renal involvement, with a progressive worsening of renal function and congestive heart failure. Unfortunately, the prognosis of cardiac amyloidosis is often very poor. Echocardiography and electrocardiography play cornerstone role in the diagnosis and management of cardiac amyloidosis. We describe a patient with multiple myeloma who was admitted to our clinic with progressive dyspnea due to cardiac amyloidosis. This case reveals an unusual manifestation of cardiac amyloidosis on electrocardiogram.
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Abstract (Original Language):
Hafif zincirli amiloidozun (AL-A) en sık klinik sunum şekli, progresif kötüleşen renal fonksiyonlar ve kalp yetersizliği ile beraber görülen renal tutulumdur. Maalesef kardiyak amiloidozun prognozu sıklıkla kötüdür. Ekokardiyografi ve elektrokardiyografi, kardiyak amiloidozun tanısı ve tedavisinin yönetiminde köĢe taĢı rol oynamaktadır. Biz, kardiyak amiloidoz nedeniyle progresif dispne ile kliniğimize baĢvuran multiple myelom‘lu bir hastayı sunduk. Bu vakada kardiyak amiloidozun elektrokardiyogramda nadir bir görünümünü tartıştık.
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