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Sturge Weber Sendromu ve Dirençli Epilepsi Nedeniyle Hemipleji Olmuş Bir Vakanın Rehabilitasyon Sonuçları

Rehabilitation Results of a Hemiparatic Subject with Sturge- Weber Syndrome and Intractable Epilepsy

Journal Name:

  • Fırat Tıp Dergisi

Publication Year:

  • 2004

Key Words:

Keywords (Original Language):

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Abstract (2. Language): 
This study presents the results of a rehabilitation program in a spastic hemiparetic subject who had undergone hemispherectomy because of Sturge- Weber syndrome and intractable epilepsy. Sturge-Weber syndrome includes unilateral cerebral cortical angiomatosis, which often leads to progressive cerebral dysfunction and epileptic seizures that are medically difficult to control. A three-year-old girl who was followed-up for 2.5 years after a diagnosis of Sturge-Weber syndrome, intractable epilepsy and right spastic hemiparesis was hospitalized at the Department of Neurosurgery for epilepsy surgery since the frequency of her seizures had increased. The functional status and quality of life of our subject, whose seizures disappeared after hemispherectomy, improved after the rehabilitation program. ©2004, Fırat Üniversitesi, Tıp Fakültesi
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Abstract (Original Language): 
Bu çalışmada Sturge Weber ve dirençli epilepsi nedeni ile hemisferektomi yapılan spastik hemiparetik bir olgunun, rehabilitasyon sonuçları sunulmaktadır. Sturge Weber sendromu, tıbbi olarak kontrolü zor olan epilepsi nöbetleri ve ilerleyici serebral fonksiyon bozukluğu ile karakterize tek taraflı kortikal serebral angiomdur. Sturge Weber Sendromu, dirençli epilepsi ve sağ spastik hemiparezi tanısı ile 2,5 yıldır takip edilen 3 yaşındaki bir kız olgu, epilepsi nöbetlerinin artması nedeniyle epilepsi cerrahisi için nöroşirurji departmanına yatırılmıştır. Çalışma sonunda; hemisferektomi sonrası nöbetleri tamamen kaybolan olgunun, rehabilitasyon programı sonrasında fonksiyonel durumunda ve yaşam kalitesinde önemli bir iyileşme görülmüştür. ©2004, Fırat Üniversitesi, Tıp Fakültesi
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  • 4
130-133
  • Turkish

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