You are here

Home » Content

BİLATERAL ANTERİOR OPERKÜLER SENDROM (FOIX-CHAVANY-MARIE SENDROMU): BİR OLGU BİLDİRİMİ

Journal Name:

  • Cerrahpaşa Tıp Dergisi

Publication Year:

  • 2001

Key Words:

Keywords (Original Language):

Author NameUniversity of AuthorFaculty of Author
Abstract (2. Language): 
Facio-pharyngo-glosso-masticatory voluntary diplegia with retained automatic movements is called Foix- Chavany-Marie syndrome. This rare syndrome is caused by bilateral lesions of the frontal operculum or their corticofugal projections. Observation.- We present a case of acute anarthria and facio-pharyngo-glosso-masticatory diplegia with automatic voluntary dissociation, i.e. bilateral anterior opercular syndrome (Foix-Chavany-Marie syndrome) as the result of two successive, right and left, strokes that caused bilateral frontal operculum damage. Though completely speechless, the patient was neither aphasic and nor apraxic. Several etiologies and the clinical and radiological features of this rare syndrome were discussed. The differential diagnosis of the syndrome from subcortical suprabulbar paralysis, peripheral lesions of the cranial nerves and vertebrobasilar ischemic strokes of the brainstem was made.
Bookmark/Search this post with
Abstract (Original Language): 
Ard arda gelişen iki inme sonrasında, bilateral frontal operküler bölge hasarına bağlı akut olarak ortaya çıkan otomatik refleks hareketler ve istemli hareket dissosiasyonu ile birlikte fasiyo-faringo-glosso- mastikator dipleji ve anartrinin saptand ığı bir Foix-Chavany-Mary sendromu olgusu sunulmaktadır. Olgumuzda pareziye bağlı konuşma fonksiyonu tamamen ortadan kalkmış ve orobukkal hareketler yapılamıyor olup, afazi veya apraksi söz konusu değildir. Oldukça nadir görülen bu sendroma neden olan çeşitli etyolojiler ile sendromun klinik ve radyolojik özellikleri tartışılmıştır. Ayırıcı tanısında yer alan subkortikal suprabulber paralizi, kranyal sinirlerin periferik lez-yonları ve beyin sap ının vertebrobaziler iskemik inmelerinden klinik açıdan farklılıkları vurgulanm ıştır.
FULL TEXT (PDF): 
PDF icon arastirmax-bilateral-anterior-operkuler-sendrom-foix-chavany-marie-sendromu-bir-olgu-bildirimi.pdf
  • 4
249-254
  • Turkish

REFERENCES

References: 

1. Weller M. Anterior opercular cortex lesions
cause dissociated lower cranial nerve palsies
and anarthria but no aphasia: Foix-Chavany-
Marie syndrome and “automatic voluntary dissociation
”. J Neurol 1993; 240: 199-208.
2. Mariani C, Spinnler H, Sterzi R, and Vallar G.
Bilateral perisylvian softenings: Bilateral anterior
opercular syndrome (Foix-Chavany-Marie
syndrome). J Neurol 1980; 223: 269-288.
3. Melo TP, Bogousslavsky J. Hemiparesis and
other types of motor weakness. In: Bogousslavsky
J, Caplan L, eds. Stroke syndromes
Part I. Cambridge University, 1995: 3-
14.
4. Campello I, Velilla I, López López A, Tapiador
MJ, Marta E, Martin Martinez J. Biopercular
lesion with inverse dissociation. Rev Neurol
1995; 23: 1056-1058.
5. Weller M, Poremba M, Dichgans J. Opercular
syndrome without opercular lesions: Foix-
Chavany-Marie syndrome in progressive supranuclear
motor system degeneration. Eur-
Arch-Psy-Neurol Sci 1990; 239: 370-372.
6. Laurent VA, Fadda G, Laigle P, Dusser A,
Leroy MV. Foix-Chavany-Marie syndrome in a
child caused by a head trauma. Rev Neurol
1999; 155: 387-390.
7. Becker PS. Developmental Foix-Chavany-Marie
syndrome: polymicrogyria or macrogyria? Ann
Neurol 1990; 27: 693-694.
8. Shevell MJ, Carmant L, Meagher VK. Developmental
bilateral perisylvian dysplasia. Pediatr
Neurol 1992; 8: 299-302.
9. Colamaria V, Sgrň V, Caraballo R, Simeone M,
Zullini E, Fontana Ezanetti R, Grimau MR,
Dalla BB. Status epilepticus in benign rolandic
epilepsy manifesting as anterior operculum
syndrome. Epilepsia 1991; 32: 329-334.
10. Graff R, Bosch EP, Stears JC, Tranel D. Developmental
Foix-Chavany-Marie syndrome in
identical twins. Ann Neurol 1986; 20: 632-635.
11. Lang C, Reichwein J, Iro H, Treig T. Foix-
Chavany-Marie syndrome: neurological, neuropsychological,
CT, MRI, and SPECT findings in
a case progressive for more than 10 years. Eur
Arch Psychiatry Neurol Sci 1989; 239: 188-193.
12. Cellerini M, Mascalchi M, Salvi F, Muscas GC,
Dal Pozzo G. MRI of congenital Foix-Chavany-
Marie syndrome. Pediatr Radiol 1995; 25: 316-
317.
13. Grattan SPJ, Hopkins IJ, Shield LK, Boldt DW.
Acute pseudobulbar palsy due to bilateral focal
cortical damage: the opercular syndrome of
Foix-Chavany-Marie. J Child Neurol 1989; 4:
131-136.
14. Broussolle E, Bakchine S, Tommasi M, Laurent
B, Bazin B, Cinotti L, Cohen L, Chazot G.
Slowly progressive anarthria with late anterior
opercular syndrome: a variant form of frontal
cortical atrophy syndromes. J Neurol Sci 1996;
144: 44-58.
15. Ianetti P, Raucci U, Basile LA, Spalice A, Parisi
P, Fariello G, Imperato C. Benign epilepsy of
childhood with centrotemporal spikes and unilateral
developmental opercular dysplasia.
Childs Nerv Syst 1994; 10: 264-269.
16. Gropman AL, Barkovich AJ, Vezina LG, Conry
JA, Dubovsky EC, Packer RJ. Pediatric congenital
bilateral perisylvian syndrome: clinical
and MRI features in 12 patients. Neyropediatrics
1997; 28: 198-203.
17. Millikan CH, McDowell F, Easton JD. Pregnancy,
oral contraceptives, and stroke. In: Millikan
CH, McDowell F, Easton JD,eds. Stroke.
Chap. 29. Lea & Febiger, 1987; 287-291.
18. Villa G, Caltagirone C. Speech suression
wthout aphasia after bilateral perisylvian softenings
(bilateral rolandic operculum damage).
Ital J Neurol Sci 1984; 5: 77-83.
19. Nisipeanu P, Rieder I, Blumen S, Korczyn AD.
Pure congenital Foix-Chavany-Marie syndrome.
Dev Med Child Neurol 1997; 39: 696-
698.
20. Colombo A, Crisi G, Guerzoni MC, Awni M,
Panzetti P. Foix-Chavany-Marie syndrome.
Case report. Riv Patol Nerv Ment 1983; 104:
145-149.
21. Asenbauer B, McEntagart M, King MD, Gallagher
P, Burke M, Farrell MA. Chronic active
destructive herpes simplex encephalitis with
recovery of viral DNA 12 years after disease
onset. Neuropediatrics 1998; 29: 120-123.
22. Grassi MP, Borella M, Clerici F, Perin C, Bini
MT, Mangoni A. Reversible bilateral opercular
syndrome secondary to AIDS-associated cerebral
toxoplasmosis. Ital J Neurol Sci 1994; 15:
115-117.
23. Sztymirska D, Jedrzejowska H. Foix-Chavany-
Marie syndrome. Neurol Neurochir Pol 1998;
32: 171-176.
24. Kobayashi S, Kunimoto M, Takeda K. A case of
Foix-Chavany-Marie syndrome and crossed
aphasia after right corona radiata infarction
with history of left hemispheric infarction. Rinsho
Shinkeigaku 1998; 38: 910-914.

Thank you for copying data from http://www.arastirmax.com