Diffuse orthohyperkeratotic keratodermia (Unna-Thost syndrome) a case report
Journal Name:
- İnönü Üniversitesi Tıp Fakültesi Dergisi
Keywords (Original Language):
Author Name | University of Author | Faculty of Author |
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Abstract (2. Language):
Palmoplantar keratodermia is a disease, which is characterized by hyperkeratosis of the palms and soles. It may be hereditary or acquired. Unna-Thost syndrome is the hereditery type palmoplantar keratodermia, inherited as autosomal dominant trait. It usually occurs in early infancy but may appear later in life.
In this case report, a patient with Unna-Thost type palmoplantar keratodermia is presented due to its rarity.
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Abstract (Original Language):
Palmoplanter keratodermiel ve ayaklarda hiperkeratozla karakterize bir hastalıktır. Herediter veya edinsel olarak gelişebilir. Unna-Thost sendromu palmoplanter keratodermilerin herediter bir tipi olup otozomal dominant olarak kalıtılır. Genellikle erken çocukluk döneminde görülür ancak yaşamın ileri dönemlerinde de başlayabilir.
Burada nadir görülmesi nedeniyle Unna-Thost tipi palmoplanter keratodermisi olan bir olgu sunulacaktır.
- 4
301-303