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BÜYÜME GERİLİĞİ OLARAK BAŞVURAN JUVENİL CREST SENDROMU

ACASE OF JUVENILE CREST SYNDROME REPRESENTING AS FAILURE TO THRIVE

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Abstract (2. Language): 
The CREST syndrome refers to the manifestations of calcinosis, Raynaud’s phenomenon, esophageal involvement, sclerodactily and telengiectasisas. Onset during childhood is very uncommon and fewer than 100 cases have been reported in the literature. We describe a 9-year-5 month girl diagnosed as CREST syndrome whose symptoms were present since 1-year-old. Since that time she had been followed as growth failure.This patient points out that growth retardation in childhood may be the initial manifestation of CREST syndrome.
Abstract (Original Language): 
CREST sendromu, kalsinozis, Raynaud fenomeni, ösafagial tutulum, sklerodaktili ve telenjiektazilerle karakterize bir hastal›kt›r. Çocukluk ça¤›nda bafllamas› oldukça nadirdir ve literatürde 100'den az olgu bildirimi mevcuttur. Bu makalede, flikayetleri 1 yafl›ndan beri olan 9 yafl 5 ayl›k CREST sendromu tan›s› alan bir k›z olgu tan›mlanm›flt›r. Olgu o tarihten itibaren geliflme gerili¤i tan›s›yla izlenmifltir. Bu olgu çocukluk ça¤›nda karfl›m›za ç›kan büyüme geliflme gerili¤i tablolar›n›n CREST sendromunun bafllang›c›na iflaret edebilece¤ini vurgulamas› aç›s›ndan dikkat çekicidir.
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