You are here

Kesintili Arkus Aorta Sendromu

Interrupted aortic arch

Journal Name:

Publication Year:

Abstract (2. Language): 
Interrupted aortic arch is defined as a complete separation of ascending and descending aorta. Our patient was classified type B whose interruption was between the left common carotid and subclavian arteries. Type B Interrupted aortic arch associated with other extracardiac and intracardiac congenital lesions is a lethal defect. Hovvever, interruption of the aotic arch in association with ventricular inversion, hypoplastic left ventricul and double inlet left ventricul is a very rare condition. We report one case whose survival was provided by primary cardiac repair,
Abstract (Original Language): 
Kesintili aort arkı sendromu, asending ve desending aortanın tamamen birbirinden ilişkisiz oluşunu tanımlar. Hastamızda sol karotis ve subklavyen arter arası kesinti olan tip B kesintili arkus aorta sendromu vardı. Tip B sıklıkla başka intra ve ekstrakardiyak anomalileri de içerir ve letal bir konjenital kardiyak anomalidir. Bununla beraber kesintili arkus aortanın hastamızda olduğu gibi ventriküler inversiyon, hipoplastik sol ventriküi ve çiftgirişili sol ventrikülle birlikteliği çok nadir bir durumdur. Kardiyak cerrahi girişim sonrası halen kliniğimizde takip edilen bir olguyu nadir görülmesi nedeni ile sunmaktayız.
53-55

REFERENCES

References: 

1. Kaulitz R, Jonas RA, van der Velde ME. Echocardİographic assesment of interrupted aortic arch. Cardiol Young 1999;.9: 562-71.
2. Schreiber C, Mazzitelli D, Haehnel JC, Lorenz HP, Meisner H. The İnterrupted aortic arch: an overwiev after 20 years of surgical treatment. Eur J Cardiothorac 1997; 12: 466-9.
3. Morrow WR, Huhta JC. Aortic arch and pulmonary artery anomalies. İn: Garson A, Bricker JT, Fisher DJ, Neish SR (editors). The science and practice of pedi-atric cardiology (2nd ed) Vol 2. Baltimore: Williams & VVîlkins Co, 1998: 1347-82.
4. VVhitley HG, Perry LW. Interrupted aortic arch. İn: Long WA (editör) Fetal & neonatal cardiology. Philadelphia: WB Saunders Company, 1990: 487-91.
5. Weinberg PM. Aortic arch anomalies. İn: Emmanouilides GC, Riemenschreider TA, Ailen HD. Gutgesell HP. Moss and Adams Heart Disease in infants, children and adolescents (5 th ed) Vol 1. Baltimore: VVilliams & VVilkins, 1995: 810-38.

6. Wong CK, Cheng CH, Lau CP, Leung WH, Chan FL. Interrupted aortic arch in an asymptomatic adult. Chest 1989; 96: 678-9.
7. Rangel A, chavez E, Espinosa I. İnterruption of the aor¬tic arch in adults. Arch Inst Cardiol Mex 199; 69: 144-8.
8. Takahashi K, Kuwahara T, Nagatsu M. İnterruption of the aortic arch at the isthmus with DiGeorge syndrome and 22q11.2 deletion. Cardiol Young 1999; 9{5): 516-8.
9. Lewin MB, Lindsay EA, Jurecic V, Goytia V, Towbrn JA, Baldini A. A genetic etiology tor interruption of the aor¬tic arch type B. Am J Cardiol 1997; 80: 493-7.
10. Schreiber C, Eicken A, Vogt M. Repair of interrupted aortic arch: results after more than 20 years. Ann Thorac Surg 2000; 70(6): 1896-9. .
11. Powell CB, Stone FM, Atkins DL, VVatson DG, Moller JH. Operative mortality and frequency of coexistent anomalies in interruption of the aortic arch. Am J Cardiol 1997; 79: 1147-8.

Thank you for copying data from http://www.arastirmax.com