You are here

Ender bir hemotoraks olgusu: Torasik Evving sarkomu

A rare case of hemothorax: Due to thoracic Evving's sarcoma

Journal Name:

Publication Year:

Keywords (Original Language):

Abstract (2. Language): 
An 11 - year old boy presented to the emergency room with severe dyspnea and left upper chest pain. The initial chest radiograph shovved a massive left pleural effusion, opacities in the left hemithorax and lytic areas İn the left 3rö rib. A thoracocentesis demonstrated a hemothorax. Despite treafment with blood tansfusions and aspiration of hemothorax, the patient's clinical status vvorsened and developed dyspnea. A thoracic computed tomograghic scan demonstrated a mass in the İntrathoracic extrapulmonary space and a lytic lesion İn the 3rd rib. A posterolateral thoracotomy was performed. Base on histologic findings, evving's sarcoma was diagnosed. He was asymptomatic throughout the 11 months follovv - up. İntrathoracic extrapulmonary thoracic Evving's sarcoma vvith spontaneous hemothroax is extremelyare.
Abstract (Original Language): 
Bir aydan beri sol üst göğüs ağrısı olan 11 yaşında erkek çocuğu şiddetli solunum sıkıntısıyla acil servise başvurdu. Çekilen akciğer radyografisi sol masif plevral efüzyonu,sol hemitoraks opasitesi ve sol 3. kotta litik alan¬ları gösterdi. Torasentezle hemotoraks demonstre edildi. Hastanın klinik durumunda kan replasmanına ve hemo¬toraks aspire edilmesine rağmen rahatlama olmadı. Bilgisayarlı toraks tomografik inceleme (BT) intratorasik ekstrapulmoner yerleşimli kitle ve 3. kotta litik lezyonun olduğu izlenimini verdi. Hastaya acil şartlarda posterolate-ral torakotomi uygulandı. Kitle göğüs duvarı ile çıkarıldı. Histolojik incelemesinde geniş alanlarda yuvarlak, hiperkromatik, nisbeten küçük hücrelerin vasküler bir stroma içerisinde yerleştikleri İzlendi. Bu bulgularla Ewing sarkomu tanısı kondu. Olgu cerrahiden sonra, 11 aylık takibinde asemptomatiktir. Masif hemotoraksla birlikte olan İntratorasik ekstrapulmoner Ewing sarkomu, oldukça enderdir.
119-123

REFERENCES

References: 

1. Pairolero C. Chest wall tumors. İn: Shields TW, Lo Cicero J, Ponn RB; eds. General Thoracic Surgery, 4th ed. Philadelphia, PA: üppincott VVİlliams & VVilkins: 2000:p.589-98.
2. Patricia M. Mc Cormack. Tumors of the chest wall İn: Joseph Aisner et al (ed): Comprehensive textbook ofthoracic oncology. 1 st ed. Pennsylvania: Lıppıncott VVİlliams & VVilkins: 1996Xp.870-9.
3. Huang SH. Ko WS, Jen YM, Lee SC, Hwang WS. İntrathoracic extrathoracic extraskeletal Ewing's sarco-ma: a case report and review ofliterature. Zhonghua Yi Xue Za Zhi (Taipei) 1993;51(6):474-8. (Abstract)
4. Daugaard S, Kamby C, Sunde LM, Myhre - Jensen O, Schiodt T. Ewing's sarcoma. A retrospective study of histoiogical and immunohistochemical factors and their relation to prognosis. Virchows Arch Pathol Anat Histopathol 1989;414(3):243-51.
5. Harrison NK, VVükinson JT O'donohue J,Hansell D, Sheppard MN, Goldstravv PG, et al. Osteochondroma of the rib: an unusual cause of haemothorax. Thorax1994:49(6):618-9.
6. Buchan KG, Zamvar V, Mandana KM, Nihal E, Kulatilake P. Jxtacardiac costal osteochondroma pre-senting as recurrent hemothorax. Eur J Cardiothorac Surg 2001 ;20(1 ):208-10.
7. Hachiya T, Okada K, Yamazaki Y, Hayasaki M, Yoshikavva S, Kubo K, et al. Pulmonary malignant fibrous histiocytoma

8. Kumagai M, Kutsuzawa T, Kondo T, Ohta Y, Yamabayashi H, İnada K, Kawana A.A case of angiosarcoma presenting as İli defined opacities on chest roentgenogram and hemothorax. Kokyu To Junkan 1993;41(8):801-4. (Abstract).
9. Kani H, Yamakawa Y, Niwa H, Kondo K. Kiriyama M. Masaoka A. A case of hamartoma originated from the chest wall. Nibon Kyobu Geka Gakkai Zasshi 1996: 44(7): 1008-11. (Abstract)
10. VVarg AA. Patterson HS, Hemstreet MP. Tiller RE. Hemothorax in a patient with asîhma. Ann Allergy 1990:64(1 ):55-7.
11. Shamberger RC, Laquaglia MP, Krailo MD, Miser JS, Pritchard DJ, Gebhart MC, et al. Ewing's sarcoma of the rib: results of an İntergroup sîudy with analysis of outcome by timing of resection. J Thorac Cardiovasc Surg 2000;119:1154-61.
12. Pairolero C. Chest VValI Reconstruction. İn: Shields TW, LoCicero J, Ponn RB; eds. General Thoracic Surgery. 4th ed. Philadeiphia. PA: Lippincott VVilliams-VVilkins; 2000:p.599-608.
13. Deschamps C, Tirnaksiz BM, Darbandi R, Trastek VF Ailen MS. Miller DL, et al. Early and long- term results of prosthetic chest wali reconstruction. J Thorac Cardivasc Surg 1999:117:588-91.

Thank you for copying data from http://www.arastirmax.com