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Pediyatride Kistik Böbre k Hastalıkları

Cystic Kidney Diseases in Pediatry

Journal Name:

  • Türk Nefroloji, Diyaliz ve Transplantasyon Dergisi

Publication Year:

  • 2007
Author NameUniversity of AuthorFaculty of Author
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Abstract (Original Language): 
KUTA (European Dialysis and Transplantation Association) verilerine göre 1976-1989 yılları arasında, son dönem böbrek yetmezliği olan 2 yaşından küçük hastaların %7'sİnde, 2-15 yaş arasındaki hastaların %10'unda polikistik böbrek hastalığı tanısı konulmuştur ti). NAPRTCS (North American Pediatric Renal Transplant Cooperative Study) kayıtlarında, böbrek nakli yapılan hastaların %3'ünde tam polikistik böbrek hastalığıdır (2). Çocukluk çağı polikistik böbrek hastalığı otozo-mal fesesİf polikistik böbrek hastalığı, otozomal dominant polikistik böbrek hastalığı, glomerülokîstik böbrek hastalığı, tüberöz skleroz ve diğer sendrom-lan kapsamaktadır. Bu makalede öncelikle otozomal resesif polikistik böbrek hastalığının klinik bulguları gözden geçirilmiş ve ayırıcı tanıda dikkate alınması gereken otozomal dominant polikistik böbrek hastalığı. mültikİsük displastik böbrek, tüberöz skleroz ve netronofitiziye değinilmiştir.
FULL TEXT (PDF): 
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  • 1
27-34
  • Turkish

REFERENCES

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