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Nefrotik Sendromun Nadir Bir Nedeni: C1q Nefropatisi

A Rare Cause of the Nephrotic Syndrome: C1q Nephropathy

Journal Name:

  • Türk Nefroloji, Diyaliz ve Transplantasyon Dergisi

Publication Year:

  • 2012
DOI: 
DOI 10.5262/tndt.2012.1002.18

Key Words:

Keywords (Original Language):

Author NameUniversity of AuthorFaculty of Author
Abstract (2. Language): 
C1q nephropathy is a rare cause of idiopathic nephrotic syndrome seen in children and young adults. Mesangial proliferation with deposition of C1q in the mesangium on immunofluorescence examination is the main pathological feature of the disease. Diagnosis is made by ruling out systemic lupus erythematosus with clinical and laboratory investigation. In this report, we discussed a patient presenting with nephrotic syndrome and C1q nephropathy with a review of the relevant literature.
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Abstract (Original Language): 
C1q nefropatisi; sıklıkla çocuklarda ve genç erişkin yaş grubunda görülen, nadir, idiyopatik nefrotik sendrom nedenlerindendir. Temel patolojik özelliği, mezengial proliferasyon ile birlikte immünfloresan değerlendirmede mezengial C1q depolanması olup; tanı için klinik ve laboratuvar bulguların varlığı yanında, sistemik lupus eritematozusun ekarte edilmesi gerekmektedir. Bu yazıda, C1q nefropatisi tanısı konulan bir olgu, literatürden gözden geçirilerek sunulmuştur.
FULL TEXT (PDF): 
PDF icon arastrmx_172977_21_pp_195-197.pdf
  • 2
195-197
  • Turkish

REFERENCES

References: 

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