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Galen ven anevrizmalı bir yenidoğan

A newborn with Galen vein aneurysm

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Abstract (2. Language): 
Galen vein aneurysm develops as a result of the presence of an arteriovenous fistula between choroidal branches of the cerebral artery and/or branches of the basilar artery and the dilated veins of the mesencephalon. Males and females are affected equally. Aneurysm of Galen vein malformation is the most common cerebrovascular malformation which is symptomatic in neonatal and infantile period. It typically causes a high-output congestive heart failure and presents with developmental delay, hydrocephalus and seizures. As a conclusion malformation of Galen vein causes progressive neurological defects due to its mass effect. Better clinical results may be achieved by using intrafistular occlusive substances in the treatment. In this paper a newborn with Galen vein aneurysm diagnosed antenatally and treated postnatally with the diagnoses of hyperdynamic heart failure and pulmonary hypertension at our clinic is presented as it is very rare
Abstract (Original Language): 
Galen ven anevrizması serebral arterin koroid dalları ve/veya baziler arter dalları ile mezensefalonun genişlemiş venleri arasında arteriyovenöz bir fistülün varlığı sonucunda, Galen venin genişlemesi ile oluşur. Kız ve erkeklerde eşit oranda görülür. Yenidoğan ve süt çocukluğu döneminde en sık semptom veren serebrovasküler patoloji Galen veni anevrizmasıdır. Tipik olarak yüksek debili konjestif kalp yetmezliğine yol açar ve gelişme geriliği, hidrosefali ve konvülziyonlarla karşımıza çıkar. Sonuçta Galen ven malformasyonu kitle etkisi ile progresif nörolojik defektlere yol açar. Tedavisinde fistül içerisi tıkayıcı maddeler kullanılarak daha iyi klinik sonuçlar alınabilmektedir. Bu yazıda antenatal takibinde Galen ven anevrizması tespit edilen, postnatal dönemde hiperdinamik kalp yetmezliği ve pulmoner hipertansiyon nedeniyle kliniğimizde takip ve tedavi edilen Galen ven anevrizmalı bir olgu nadir görüldüğü için sunulmuştur
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REFERENCES

References: 

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