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Hirayama Hastalığı (Monomelik Amyotrofi)

Hirayama Disease (Monomelic Amyotrophy)

Journal Name:

  • Fırat Tıp Dergisi

Publication Year:

  • 2008

Key Words:

Keywords (Original Language):

Author Name
Abstract (2. Language): 
Hirayama Disease (HD) is a benign lower motor neuron disorder in the young with male preponderance. It is characterized by insidious onset and progressive weakness and wasting of a distal extremity . Generally, this disease is considered a 'benign' and non-progressive motor neuron disease, which stabilizes within five years of onset.We describe a 23-year-old famele patient who experienced progressive amyotrophy with no sensorial abnormality. ©2008, Firat University, Medical Faculty.
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Abstract (Original Language): 
Hirayama Hastalığı (HH), genç erkeklerde daha sık görülen benign bir alt motor nöron hastalığıdır. Distal ekstremiteyi tutan ilerleyici güçsüzlük ve sinsi başlangıç ile karekterizedir. Genellikle başlangıcından sonra 5 yıl içinde stabilize olan, benign ve nonprogresif bir hastalık olarak kabul edilir. Biz bu bildiride duysal yakınmanın eşlik etmediği progresif amyotrofi bulguları olan 23 yaşında bir kadın hastayı sunuyoruz.©2008, Fırat Üniversitesi, Tıp Fakültesi
FULL TEXT (PDF): 
PDF icon arastrmx_135291_13_pp_274-276.pdf
  • 4
274-276
  • Turkish

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