Buradasınız

Konjenital diyafragma evantrasyonu: olgu sunumu

Congenital diaphragma evantration: a case report

Journal Name:

Publication Year:

Keywords (Original Language):

Abstract (2. Language): 
Diaphragmatic eventration is characterized by a permanent elevation of diaphragma, which can not complete its muscularization during gestation. Intraabdominal organs at the affected side compress lungs due to loose diaphragma and impair pulmonary functions, and problems related to the organs at the contralateral side may occur due to the mediastinal shift. Patients may present with diverse complaints, ranging from mild gastrointestinal symptoms such as nausea and vomiting to life-threatening respiratory distress. Although it can be asymptomatic, it may cause recurrent pneumonia impairing lung inflation. We herein report a case with congenital diaphragmatic eventration presenting with recurrent pneumonia.
Abstract (Original Language): 
Diyafragma evantrasyonu, gebelik esnasında yeterli müsküler gelişimini sağlayamayan diyafragmanın yüksek yerleşimli olması ile karakterizedir. Karındaki organlar gevşek yapılı diyafragma etkisiyle akciğerlere baskı yapmakta, pulmoner fonksiyonları etkilemekte ve mediyastinal kayma sonucunda etkilenen tarafın karşı tarafındaki organlara ait problemler ortaya çıkmaktadır. Hastalar bulantı ve kusma gibi hafif gastrointestinal semptomlardan hayatı tehdit edici solunum sıkıntısı tablosuna kadar çok değişik yakınmalarla başvurabilir. Asemptomatik seyredebildiği gibi, akciğerin havalanmasını bozarak tekrarlayan pnömonilere neden olabilmektedir. Bu makalede tekrarlayan pnömoni tablosuyla seyreden konjenital diyafragma evantrasyonlu bir olgu sunulmaktadır.
250-252

REFERENCES

References: 

1. Tsugawa C, Kimura K, Nishijima E, Muraji T,
Yamaguchi M. Diaphragmatic eventration in infants and
children: is conservative treatment justified? J Ped Surg
1997; 32: 1643-1644.
2. Mouroux J, Venissac N, Leo F, Alifano M, Guillot F.
Surgical treatment of diaphragmatic eventration using
video-assisted thoracic surgery: a prospective study. Ann
Thorac Surg 2005; 79: 308-312.
3. Wayne ER, Campbell JB, Burrington JD, Davis WS.
Eventration of the diaphragm. J Pediatr Surg 1974; 9: 643-
651.
4. Jurcak-Zaleski S, Comstock CH, Kirk JS. Eventration of
the diaphragm. Prenatal diagnosis. J Ultrasound Med
1990; 9: 351-354.
5. Steiner RD, Dignan PStJ, Hopkin RJ, Kozielski R, Bove
KE. Combination of diaphragmatic eventration and
microphtalmia/anophtalmia is probably nonrandom. Am
J Med Genet 2002; 108: 45-50.
6. Yazýcý M, Karaca I, Arikan A, et al. Congenital eventration
of the diaphragm in children: 25 years' experience in three
pediatric surgery centers. Eur J Pediatr Surg 2003; 13:
298-301.
7. Yang IJ. Left diaphragmatic eventration diagnosed as congenital diaphragmatic hernia by prenatal sonography. J
Clin Ultrasound 2003; 31: 214-217.
8. Eren S, Ceviz N, Alper F. Congenital diaphragmatic
eventration as a cause of anterior mediastinal mass in the
children: imaging modalities and literature review. Eur J
Radiol 2004; 51: 85-90.
9. Becmeur F, Talon I, Schaarschmidt K, et al. Thoracoscopic diaphragmatic eventration repair in children: about
10 cases. J Pediatr Surg 2005; 40: 1712-1715.

Thank you for copying data from http://www.arastirmax.com