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Banti’s syndrome in a young male

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Abstract (2. Language): 
Banti’s syndrome is a rare disease which is characterised by ascites, splenomegaly and portal hypertension without coexisting cirrhosis of liver. There is no geographical predilection for the disease. It is usually occurs around 3rd to 4th decade of life. Here we report a case of a 16 year old boy who presented with ascites, massive splenomegaly and pancytopenia. CECT abdomen revealed thrombosed portal radicals with normal liver. He was subsequently diagnosed to have Banti’s syndrome. Through this case we deduce that Banti’s syndrome must be considered in cases with portal hypertension though they may be of younger age group.
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