A Klippel-Trenaunay Syndrome With Generalized Capillary Hemangioma and Trigger Finger
Journal Name:
- İnönü Üniversitesi Tıp Fakültesi Dergisi
Keywords (Original Language):
| Author Name | University of Author | Faculty of Author |
|---|---|---|
Abstract (2. Language):
Klippel-Trenaunay Syndrome (KTS) is a rare disorder characterized by deep venous abnormalities, superficial varices,
hemangiomas as well as hypertrophy of the soft tissue and the bone. We report a two and half year old girl diagnosed
as KTS presenting with generalised capillary hemangiomas, dorsal edema on left foot , hipertrophy and trigger finger
deformity of right second, third and forth fingers.
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Abstract (Original Language):
Klippel-Trenaunay Sendromu (KTS), derin ven anormallikleri, yüzeyel varisler, hemanjiyomlar, kemik ve yumuşak
dokunun hipertrofisi ile karakterize nadir görülen bir sendromdur. Bildirimizde yaygın kapiller hemanjiom, sol ayak
sırtında ödem ve sağ el iki, üç ve dördüncü parmaklarda şişlik ve tetik parmak deformitesi bulunan 2,5 yaşında KTS u
olan bir kız olgu sunulmaktadır.
FULL TEXT (PDF):
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379-381