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Stargardt makülar distrofisi

Stargardt's Macular Dystrophy

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Abstract (2. Language): 
Stargardt's macular dystrophy is primarily disorders of photoreceptor's cells (cone-rod) and pigment epithelium. It affects male and female equally, especially in the first and second decade of life and leads to bilateral, symmetric loss of visual acuity. The transmission of inheritance is frequently recessive trait. The purpose of this report is to present and review Stargardt's macular disease (that was detected in 5 siblings of a family) under the light of new literature studies. [Journal of Turgut Özal Medical Center 1996;3(2):113-115]
Abstract (Original Language): 
Stargardt maküler distrofisi primer olarak fotoreseptör hücrelerinin (kon-rod) ve pigment epitelyumunun bozukluğudur. Özellikle ilk ve ikinci dekadda kadın ve erkekleri eşit olarak tutar ve bilateral, simetrik görme keskinliği kaybına yol açar. Sıklıkla resesif geçişlidir. Bu vaka bildiriminin amacı bir ailede 5 kardeşte saptanan Stargardt maküler hastalığını yeni literatür bilgileri ışığı altında sunmak ve gözden geçirmektir. [Turgut Özal Tıp Merkezi Dergisi 1996;3(2):113-115]
113-115

REFERENCES

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