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ATİPİK ÖZELLİKLİ SANTRO-TEMPORAL DİKENLİ BENİGN ÇOCUKLUK EPİLEPSİLİ BİR VAKA

A case of benign epilepsy with centro-temporal spikes with atypical features

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Abstract (2. Language): 
Benign epilepsy with centro-temporal spikes still remains the model of the benign localization-related epilepsies of childhood. However, its EEG and clinical features are variable and many of its aspects can be debated: manifestations of seizures, localization of the focal EEG paroksisms, existence of associated generalized abnormalities, long-term outcome. Other important problems consist of the relationship with other types of epilepsy and the significance of the EEG pattern when it is present in other situations. We disscussed this subject with a case of benign epilepsy with centro-temporal spikes, who had focal neurologic deficit and paroxysmal discharges that were highly activated during sleep.
Abstract (Original Language): 
Lokalize idiopatik epilepsilerden Santro-Temporal Dikenli Benign Çocukluk Epilepsisi (Benign Epilepsy with Centro-Temporal Spikes) ile ilgili tanımlar çok açık olmasına rağmen bazen klinik pratikte hastaya yaklaşımda zorluklarla karşılaşılır. Bunlar nöbet semptomatolojisi, foka/ EEG paroksismlerinin lokalizasyonu, generalize EEG paroksismlerinin birlikte olması ve klinik seyir başlıkları altında toplanabilmektedir Ayrıca bu sendromun diğer epilepsilerle ortak yönleri, sentro-temporal dikenlerin epilepsi ile birlikte olan veya olmayan diğer durumlarda görülmesi ve genetik predispozisyon yönü ile idiopatik jenera/ize epilepsi/er ile ilişkileri gibi konular da tam olarak netleşmemiştir1. Makalede Santro-Temporal Dikenli Benign Çocukluk Epilepsisi ile uyumlu kliniği olan, anoksik doğum öykülü, lateralize nörolojik defisitli, tedaviye dirençli nöbetleri olan, foka/ EEG paroksism/eri uyku aktivasyonu ile farklı özellikler gösteren bir vaka değerlendirildi.
285-288

REFERENCES

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