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"COMMON VARIABLE" IMMUN YETMEZLİK: OLGU SUNUMU

Common variable ımmun deficieney: case report

Journal Name:

  • İstanbul Tıp Fakültesi Dergisi

Publication Year:

  • 1999

Key Words:

Keywords (Original Language):

Author NameUniversity of AuthorFaculty of Author
Abstract (2. Language): 
CVID which is one of thc most important primary immune deficieney disorders is characterized by B-lymphocyte deficieney, defeetive antibody response to various antigenİc stimult and suspectibility to infeetions. It is diagnosed most frequently in patients 6-ÎO years old and 26-30 years old. In patients wİth CVID, the risk of developing autoimmune dİsease is inereased. The most frequent cause of death is infeetions. Prognosis is better if theraphy is began before signifıcant structural organ damage oecurs. Herein we present four cases of CVID, and review the clinical laboratory and clinical features ofCVTÛ.
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Abstract (Original Language): 
Primer immün yetersizlik hastalıkları içinde çok önemli bir yeri olan "conımon variable İmmunodefİcİency" B-lenfosit yetersizliği ile karakterize, pek çok antijene karşı antikor cevabının defektif olduğu, infeksiyonlara eğilimin arttığı bir tablodur. Tanı konulma yaşı en sık 6-10 ve 26-30 yaşlardır. CVID'li hastalarda otoimmün hastalığa yakalanma oranı artmıştır. En sık ölüm sebebi enfeksiyonlardır. Yapısal organ hasarı gelişmeden tedaviye başlanırsa prognoz iyidir. Bu yazıda dört vakanın klinik ve laboratuar Özelliklerini özetleyerek CVID'i gözden geçireceğiz.
FULL TEXT (PDF): 
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  • 3
320-324
  • Turkish

REFERENCES

References: 

KAYNAKLAR
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