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VACTERL BİRLİKTELİĞİ VE POTTER SEKANSI

VACTERL ASSOCIATION WITH POTTER SEQUENCE

Journal Name:

  • İstanbul Tıp Fakültesi Dergisi

Publication Year:

  • 2010

Key Words:

Keywords (Original Language):

Author NameUniversity of AuthorFaculty of Author
Abstract (2. Language): 
Upper urinary system involvement is common in VACTERL association. However cases, reported in literature, have nonserious renal abnormalities and generally have a good outcome. We report a neonate who died shortly after birth, having both VACTERL association and Potter sequence due to cystic renal dysplasia. This unusual combination is extremely rare. We recommend investigating Potter sequence in the spectrum of congenital anomalies with the VACTERL association.
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Abstract (Original Language): 
VACTERL birlikteliğinde üst üriner sistem tutulumu sık görülür. Buna karĢın literatürde ki vakalarda ciddi olmayan ve genelde prognozu iyi olan böbrek tutulumu görülmektedir. Bu yazıda, doğumdan hemen sonra ölen, kistik renal displazi ve Potter sekansı ile VACTERL birlikteliği gösteren bir yenidoğan vakası sunulmuĢtur. Bu birliktelik oldukça nadir görülmektedir. VACTERL birlikteliği olan konjenital anomalilerde Potter sekansının da araĢtırılmasını önermekteyiz.
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  • 2
58-60
  • English

REFERENCES

References: 

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