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Kesintili Arkus Aorta Sendromu

Interrupted aortic arch

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Abstract (2. Language): 
Interrupted aortic arch is defined as a complete separation of ascending and descending aorta. Our patient was classified type B whose interruption was between the left common carotid and subclavian arteries. Type B Interrupted aortic arch associated with other extracardiac and intracardiac congenital lesions is a lethal defect. Hovvever, interruption of the aotic arch in association with ventricular inversion, hypoplastic left ventricul and double inlet left ventricul is a very rare condition. We report one case whose survival was provided by primary cardiac repair,
Abstract (Original Language): 
Kesintili aort arkı sendromu, asending ve desending aortanın tamamen birbirinden ilişkisiz oluşunu tanımlar. Hastamızda sol karotis ve subklavyen arter arası kesinti olan tip B kesintili arkus aorta sendromu vardı. Tip B sıklıkla başka intra ve ekstrakardiyak anomalileri de içerir ve letal bir konjenital kardiyak anomalidir. Bununla beraber kesintili arkus aortanın hastamızda olduğu gibi ventriküler inversiyon, hipoplastik sol ventriküi ve çiftgirişili sol ventrikülle birlikteliği çok nadir bir durumdur. Kardiyak cerrahi girişim sonrası halen kliniğimizde takip edilen bir olguyu nadir görülmesi nedeni ile sunmaktayız.
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REFERENCES

References: 

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