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Fallot Tetralojisindeki Cerrahi Sonuçlarımız

Our Surgıcal Results of Tetralogy of Fallot

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Abstract (2. Language): 
The aim of this study is to evulate our surgical results of Tetralogy of Fallot. Between 2001–2009, 35 patients with Tetralogy of Fallot underwent to total correction at our department. Five of them had Down syndrome (%14.2), 3 had patent ductus arteriousus (%8.5), 2 had pulmonary atresia (%5.7), 1 had hypothyroidism (%2.8) and 1 had coronary artery anomaly (%2.8). Five patients had Blalock-Tausing shunt in their medical history. Transannular approach was avoided because of causing pulmonary valve insufficiency in late period, but it was obliged to apply in 12 patients. Early mortality occured in 3 cases (%8.5) after repair. Twenty three patients were followed for mean 6.7 years. One patient with pulmonary gradient underwent reoperation at postoperative 15th month and died due to multiple organ failure. There were no complet atrioventricular block and disrhythm in long term. Second degree pulmonary insufficiency that was developed in 12 patients who underwent transannular patch closure was followed up to day. We think that ventricular septal defect and infundibular stenosis could be corrected via transatrial approach, if necessary via transpulmonar approach and in long term, pulmonary insufficiency and right ventricular disfunction could be prevented.
Abstract (Original Language): 
Bu çalışmanın amacı, Fallot tetralojisinde (FT) tam düzeltme sonrası, cerrahi sonuçlarımızın değerlendirilmesidir. Kliniğimizde 2001–2009 yılları arasında 35 hasta, FT tanısıyla operasyona alındı. 5(%14.2) hastada Down sendromu, 3(%8.5) hastada patent duktus arteriozus, 2(%5.7) hastada pulmoner atrezi, 1 (% 2.8)hastada hipotroidi ve 1(%2.8) hastada koroner arter anomalisi mevcuttu. Ayrıca 5 hastaya daha önceden kliniğimizde modifiye Blalock-Tausing şant işlemi yapılmıştı. Komplet tamir yapılan hastaların geç dönemlerinde pulmoner kapakta yetmezlik oluşturmamak için transanuler girişim sınırlı yapılmakla beraber, 12(%34.2) hastada transanüler yama ile tamir uygulamak zorunda kalındı. Tamirden sonra erken mortalite 3(%8.5) hastada gelişti. 23 hasta ortalama 6.7 yıl süreyle takip edildi. Bir hasta, pulmoner gradient nedeniyle 15. ayda reoperasyona alındı, ancak multiorgan yetmezliğinden kaybedildi. Komplet atrioventriküler blok ve geç devre disritmi görülmedi. Transanüler yama yerleştirilen 12 hastada gelişen 2˚ pulmoner yetmezlikler izlemde kaldı. VSD ve infundibuler stenozun transatriyal yolla, gerekirse transpulmoner yolla düzeltilebileceği ve uzun dönemde de pulmoner yetmezlik ve sağ ventrikül disfonksiyonunun engellenebileceği düşüncesindeyiz.
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