Journal Name:
- Uluslararası İnsan Bilimleri Dergisi
Keywords (Original Language):
| Author Name | University of Author | Faculty of Author |
|---|---|---|
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Abstract (Original Language):
Objective: Introducing acute intermittent porphyria disease and investigating the communication
techniques for acute intermittent porphyria patients who have tracheostomy
Case Report: 26 years old woman patient consulted to the hospital when she was 13 years old with
nausea and vomiting complaints. In 2008, because of respiratory arrest, tracheostomy was
implemented to the patient who had acute intermittent porphyria diagnose. The patient had two
bullous lesions on the left hand and hyperpigmentation’s on the face and legs. As a result of
metabolic acidosis (because of urine disease), the patient was taken to dialysis. After six months of
dialysis, hypernatremia was found in the laboratory tests (Na: 85).Period of acute crisis developed
In the patient with hypertension, atrophy in the muscles, fainting, abdominal pain, nausea,
vomiting and diarrhea. Because of serious diarrhea, TPN was started for the patient who was fed
with gavage before. Laboratory test results are Na:126, K:8.1, BUN:23.83, Urine:51,
Creatinine:0.94, Leukocyte:20.4, erytrocyte:2.22, Hb:6.87g/dl, Hct: %20.9, Plt:106.
Result: It is really difficult to communicate with these patients with lifespan limited because of an
extremely severe clinical condition and tracheostomy.
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