You are here

Home » Content

PAPILLON LEFEVRE SENDROMU : PATOLOJİK, HEMATOLO FÎK MIKROBIYOLOJIK VE RADYOLOJİK SONUÇLARIN DEĞERLENDİRİLMESİ (IKI OLGU NEDENİYLE )

PATHOLOGICAL, HEMATOLOGICAL , MICROBIOLOGICAL AND RADIOLOGICAL EVALUATION OK TWO PATIENTS WITH PAPILLON-LEFEVRE SYNDROMS

Journal Name:

  • Atatürk Üniversitesi Diş Hekimliği Fakültesi Dergisi

Publication Year:

  • 1999

Key Words:

Keywords (Original Language):

Author NameUniversity of AuthorFaculty of Author
Abstract (2. Language): 
Papillon-Lxfevre Syndrome (PLS) is considered to be transmiilcd ys an autosomal recessive trait. The syndrome is estimated to have a frequency of 1 to 4 million. Consanguinity between parents was reported in one-third of eases studied. PLS is mainly characterized by hyperkeratosis of the palms mid soles and by extensive periodontal destruction , which causes early 'loss of the primary and permanent teedh. Two patients were included in the study , who were 4 and 5 years old , were siblings, and complained early loss of teeth. They were diagnosed as PLS. There was no pain in palms and soles in the patients because of skin disease. Both patienis were examined pathologically , hcmalologically and microhiologicalJy. The results were evauialcd.
Bookmark/Search this post with
Abstract (Original Language): 
Papülon-ljcftvrc Sendromu (PLS) otozoma] rescsıf çeçi-sli ve milyonda 1-4 oranında görülen bir sendromdtir Rapor edilen vakaların İ1V tinde ebeveynlerin kan akrabalığı tespit edilmiştir. Sendromnn iki karakteristik özellini ; ayrıç idleri , ayak tabanlarında hiperkçratozis vc yaygın periodontal ataşmart kaybı ile karakterize süt vc daimi dişlerin erken kaybıdır. Dişlerinin erken kaybedilmesi şikayet] eriyle müracaat eden 4 vc 5 yaşlarındaki iki kardeş incelendi. Hastalık PLS ofarafc teşhis edildi, Hastalarda A ve ayaklarımdaki deri bulgularından dolayı belirgin aşn şikayeti yoktu. Hastalarda patolojik , hematolojik ve mikrobiyolojik tetkikler yapıldı, sonuçlar değerlendi rildi.
FULL TEXT (PDF): 
PDF icon arastirmax-papillon-lefevre-sendromu-patolojik-hematolo-fik-mikrobiyolojik-radyolojik-sonuclarin-degerlendirilmesi-iki-olgu-nedeniyle.pdf
  • 2
86-93
  • Turkish

REFERENCES

References: 

t-Baer P.N.. Mc
Donal
d R.E. Suggested Mode of Periodontal Therapy for Patients with PapillonT^efevre Syndrome , Pcriodont Case Rep. 198]; 3: I -10
2- Brown RS.Hays GL. Flaitz CM., O' Neill PA.. Abramovitch K. and White RR,, Genera! A possible Lite onset variation of Papillon Tjefevre Syndrome ; Report of 3 cases, J .Periodontal 1993;64:379-386
3- E1 Darouli MA, Al Raubaie SM, Eiadn MA, Papillon I jefevre Syndrome .Successful treatment with oral retinoids in three patients , Int J Dermatol 1988"; 27: 63-66
4- Eronal N., Uçar F, Kiline G. Papillondjcfevre Syndrome : Treatment of two cases with a clinical microbiological investigation . J. Clinic. Pediatr Dentistry -1992:17:99-104
5- Fardal O , Drangsholt E , Olseıı I . Palmar Plantar Keratosis and IJmısııal Periodontal Findings. J. Clin Periodontal . 1998 ; 25 : 181-184
6- Fjratli E..TÜZÜJ1 B., Efcoğlu A. Papillon 4.efevre Svndromc , Analysis of Neutrophil Chemotaxis . J. Periodontal 1996 : 67 ; 617-620
7- Glenwright HD,Rock WP. Papillon-Lefevrc Syndrome. A discussion of actologv and a case rcjrort . Br. Dent J. 1990:168:27-29
8- Gorlin RJ, Pindborg JJ, Cohen MM In: Syndromes of (he Head and Neck ,2nd cd New York : Me Ontw -Hill Book Co; 1979
9- Oorlin RJ, Sedano H. and Anderson- VF. The syndrome of pal mar-pi anlar hyperkeratosis and premature periodontal destruction of the teeth . J. Pediatr 1964 : 65 : 895-908- In : Tinanoff NTcmpro P., Madcrazo E.G. Dental treatment of Papillon-Ijefevre Syndrome : !5-year follow up. J. Clin Periodontal 1995^2:609-12.
1Q-Hanckc E.Thc Papillon-I ycfcvre Syndrome : Keratosis palunoplanlaris with periodonlopaty : Report of case and review of the cases in the literature . Hum Genetic 1979: 51:1-35
11-Kattah F.N.. Rawaahdch M.A., Yassin O.M., Al-Momani A.S. and AJ-Ubasi M.M. Papillon-Lefevre Svndrome : A Review of The Literature and Report of 4 cases .1 Periodontal 1995 ; 66: 413-420 '
92
Atatürk Üniv.D.5 Hck.Fak.Derg. Cilt;9. Sayı:2, Sayfa:S6-93,1999
KIRZIOÖKU, GÜNIJOĞDU. ŞİMŞEK
!2-joshı HN. Dayal FK, Kansagra P.T. Papiflon-fjefcvre Syndrome :Rcport of case . ASDC J. Dent Child . 1985,51:461^463
13- Kdlum RE. Papillon-Lefevre
syndrom
e in four siblings treated with Etretinate . Int J Dermatol t989: 28: 605 60S
14- LL HKJ, Lin CT, Kwan HW. Treatment of a patient with Papillon-Lefevre Syndrome .A case report . J. Periodontal 1987:58:789-793
1
5- Lıındgreıı T f Rcavcrls S, Papapanoti PN, Dahlen G, Subgingival Microbial profile of Papillon - Lefevre patients assessed by DNA-probes. J. Clin Periodontal 1998 ; 25: 624- 629
16- Mundford AG. Papillon-Lefevre Syndrome .Report of two eases in the same familv- J- Am Dent Assoc 1976;93:121-124
17- Page R.C., Beatty P., Waldrop TC. Molecular basis for the functional abnormality in neutrophils from patients with generalized prepubertal periodontitis . J. Periodontites. 1987; 22: 182-183
18- Preus PL, Gjermo P., Clinical management of prepubertal periodontitis in 2 siblings with Papillon
Lefevre Syndrome J, Clin Periodontal 1987 ; 14:156-160
19- Preus HR, Rapidly destructive periodontitis of Papillon-Lefevre Syndrome Result of treatment based on Laboratory and clinical observetions. of 2 cases , J. Clinical
Periodontal 1988:15:639-643
20- Shoshan S.pinkelsteın S. . Rosenzweig K.A., Disc electrophoretic pattern of gingival collogen isolated from a patient with palmoplantar hyperkeratosis. J Pcriodont Res 1970; 5 255
21- Sloan P. Soamcs JV. Murray JJ. Jenkins WMM. Hlstopathological and ultrastruclura! findings in a case of Papillon Lefevre Syndrome. I Periodontal 1984; 55: 482-485
22- Tinanoff N,Tanzcr JM, Koruman S, Moderazo EG, Treatment of the periodontal component of Papillon-Lefevre Syndrome .J. Clin Periodontal 1986;13;6 -10
23- Van Dyke TK , Hoop GA . Neutrophil function and the oral disease . Crit Rev Oral Biol Med . 1990; I; 117-133
24- Van Dyke TE, Taubman MA, hbereole JL ,et al. The Papillon-Ixtcvrc Syndrome: Neutrophil dysfunction with severe periodontal disease .Clin Iramunopathol 1984:31:419-429
25- Wilktt. L., Gabriel S. Kozma C and BotLomley W. Papillon-Lefevrc : Report of a case . J. Oral Medicine 1985 ; 40: 43-45

Thank you for copying data from http://www.arastirmax.com