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NADİR BİR HİPOKALSEMİ NEDENİ: FAHR HASTALIĞI

RARE CAUSE OF HYPOCALCEMİA: FAHR'S DISEASE

Journal Name:

  • İstanbul Tıp Fakültesi Dergisi

Publication Year:

  • 2010

Key Words:

Keywords (Original Language):

Author Name
Abstract (2. Language): 
Fahr’s disease is a rare neurological disorder characterized by bilateral basal ganglia calcinosis. Calcifications cause obliteration in micro vessels, neuronal degeneration and gliosis accumulating bilaterally at the basal ganglia, thalamus, centrum semiovale and the dentate nucleus. The most used diagnostic method is cranial tomography to determine the calcifications. Fahr’s disease presents sporadically, inheritedly or secondarily (tumor, inflammation, hypoxia, endocrine, toxic, metabolic, degenerative, malabsorbtive). We want to emphasize the consequence of this syndrome for the patients presenting with hypoparathyroidism.
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Abstract (Original Language): 
Fahr hastalığı, bilateral bazal ganglionlarda kalsinozis tablosudur. Kalsiyum; kapillerler, arterioller, küçük venler ve perivasküler alanlarda birikir ve kraniyal mikrodamarlarda obliterasyon, damar çevresinde nöronal dejenerasyon ve gliozise sebep olur. Kalsifikasyonlar çoğunlukla simetrik olarak dentat çekirdek, bazal ganglion, talamus ve centrum semiovalede görülür. Tanıda, kalsiyum birikimlerini göstermede en sık kullanılan inceleme yöntemi kranial BT’dir. Etiyolojik olarak Fahr hastalığı, ailevi, sporadik veya sekonder (enflamatuar, tümoral, hipoksik, vasküler, endokrin, toksik, metabolik, dejeneratif, malabsorptif) olabilir. Biz bu nadir görülen sendromu hipoparatiroidi kliniği ile baĢvuran hastalarda akılda tutulması amacıyla tartıĢmaya sunuyoruz
FULL TEXT (PDF): 
PDF icon arastirmax-nadir-bir-hipokalsemi-nedeni-fahr-hastaligi.pdf
  • 3
82-84
  • Turkish

REFERENCES

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