Buradasınız

Spina Bifida Hastalığında Görülen Ortopedik Sorunlara Genel Yaklaşım ve Tedavi Prensipleri

GENERAL APPROACH AND TREATMENT TO ORTHOPEDIC PROBLEMS IN PATIENTS WITH SPINA BIFIDA

Journal Name:

Publication Year:

Abstract (2. Language): 
Spina Bifida (spina bifida aperta = spina bifida cystica = myelomeningosel, spinal dysrafism), is a special developmen¬tal disorder in any part of the spinal cord. It is the second most common neuromuscular disorder in children after cerebral palsy. The major problem is the closure defect at the midline of the primitive structure called neural placode while taking the form of a tube. As a result, bone tissue loss occurs in a region at the back of the vertebral column. Malformations occur throughout the central nervous system and also meta¬bolic disorders can be seen. Motor disfunction is the most common clinical problem that figures out as paraplegia and paraparesia. Several orthopedic problems are seen in almost all of the children with spina bifida. Vertebral disorders, lower extremity deformities and joint contractures are the most common problems. Multidisciplinary treatment should focus on solving the problems of the patient, and orthopedic treat¬ment is the most important part of it. The aim of the ortho¬pedic therapy as a part of the multidisciplinary approach is to let the child gain optimum mobility permit the level of the lesion permits and prevent complications.
Abstract (Original Language): 
Spina bifida (spina bifida aperta = spina bifida cystica = miyelomeningosel, spinal disrafizm), omuriliği n herhangi bir bölgesinin bozuk gelişimidir. Çocukluk döneminde, nöromüsküler fonksiyon bozukluğu yaratan hastalıklar arasında serebral palsiden sonra ikinci sırada gelir. Temel sorun, nöral plakod adı verilen ilkel yapı, omuriliği oluşturma amacıyla tüp şeklini alırken orta hatta meydana gelen kapanma eksikliğidir. Bunun sonucunda, omurga kanalının arkasında bir bölgede kemik boşluğu ortaya çıkar. Spina bifi-dalı bebeklerde merkezi sinir sistemi bozuklukları yanında metabolik birçok bozukluk ta görülür. Motor disfonksiyon en sık rastlanan klinik bulgudur; parapleji veya paraparezi şeklinde kendini gösterir. Spina bifidalı çocukların hemen hepsinde çeşitli ortopedik problemler görülür. Omurga, alt ekstremite deformiteleri ve eklem kontraktürleri en sık görülenlerdir. Mültidisipliner yaklaşım çocuğun problemlerini çözmeye odaklanmalıdır; ortopedi, bu yaklaşımda önemli bir yer tutar: Ortopedik tedavinin hedefi çocuğa tutulum seviyesinin izin vereceği optimum mobiliteyi kazandırmak ve komplikasyonları engellemektir.
125-131

REFERENCES

References: 

1. Dias L. Myelomeningocele. Campbell's Operative Orthopaedic'te. Ed. Canale T, 9. baskı. Vol 4. St Louis, Mosby, 1998; 4018-36.
2. Broughton NS, Menelaus MB. Menelaus' Orthopaedic Management of Spina Bifida Cystica. 3. Baskı London, WB Saunders, 1998; 111-4.
3.
Özara
s N, Yalçın S. Spina Bifida Tedavi ve Rehabilitasyon., İstanbul, Nobel Tıp Kitapevleri, 2000; 130.
4. MRC Vitamin Study Research Group. Prevention of neural tube defects: Results of the Medical Research Council Vitamin Study. Lancet 1991; 338: 131.
5. Hull W, Moe JH, Winter RB. Spinal deformity in myelomeningocele: natural history, evaluation and treatment. J Bone Joint Surg 1974; 56A: 1767-73.
6. Banta JV, Hamada JS. Natural history of kyphotic deformity on myelomeningocele. J Bone Joint Surg 1976; 58A: 279.
7. Sarwark JF. Spina Bifida. Pediatr Clin North Am 1996; 43(5): 1151-8.
8. Hall JE, Poitras B. The management of kyphosis in patients with myelomeningocele. Clin Orthop 1977; 128: 33-9.
9. Lintner SA, Lindseth RE. Kyphotic deformity in patients who have a myelomeningocele. Operative treatment and long-term follow-up. J Bone Joint Surg 1994; 76A: 1301-8.
10. Sharrard WJW. The orthopaedic surgery of spina bifida. Clin Orthop
1973; 92: 195-201.
11. Torode IP, Godette G. A new method of fixation myelomeningocele
kyphosis. J Pediatr Orthop 1995; 15: 202-7.
130 |
Bezer M ve ark. | Spina Bifida Hastalığında Görülen Ortopedik Sorunlara Genel Yaklaşım ve Tedavi Prensipleri
12. Broughton NS, Menelaus MB, Cole WG, Shurtleff DB. The natural history of hip deformity in myelomeningocele. J Bone Joint Surg 1993;
75B: 760-5.
13. Alman BA, Bhandari M, Wright JG. Function of dislocated hips in children with lower level spina bifida. J Bone Joint Surg 1996; 78B: 294-8.
14. Brinker MR, Rosenfeld SR, Feiwell E, Granger SP, Mitchell DC,
Rice JC. Myelomeningocele at the sacral level: Long-term outcome in adults. J Bone Joint Surg 1994; 76A: 1293.
15. Fraser RK, Bourke HM, Broughton NS, Menelaus MB. Unilateral dis¬location of the hip in spina bifida. A long-term follow-up. J Bone Joint
Surg 1995; 77B: 615-21.
16. Carroll NC. Assesment and management of the lower extremity in
myelodysplasia. Orthop Clin North Am 1987; 18: 709-19.
17. Frawley PA, Borughton NS, Menelaus MB. The incidence of foot deformities in low level spina bifida patients. J Pediatr Orthop 1998;
18(3): 312-3.

Thank you for copying data from http://www.arastirmax.com