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Çocuklarda Wilson Hastalığı

Wilson Disease in Childhood

Journal Name:

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Author NameUniversity of Author
Abstract (2. Language): 
Wilson disease should be considered in every pediatric patient with liver disease of unknown etiology. Early diagnosis and therapy prevent progression of disease and assure normal life expectancy. Lifelong copper chelation or zinc therapy with cupper deficient diet is mandatory.
Abstract (Original Language): 
Etyolojisi bilinmeyen karaciğer hastalığı olan her çocukta, özellikle akraba evliliği varsa Wilson hastalığı araştırılmalıdır. Erken tanı bu çocuklara en azından hastalığın ilerlemesini durdurarak yaşam şansı verecek veya normal bir yaşam sağlayacaktır. Bu çocuklarda bakırdan fakir diyetle birlikte yaşam boyu şelasyon veya çinko tedavisi gereklidir.
163-170

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