GRANULOCYTIC SARCOMAWHICH EMERGES BEFORE THE ACUTE MYELOID LEUKEMIAAND IS CONFUSED WITH LYMPHOMA
Journal Name:
- İstanbul Tıp Fakültesi Dergisi
Keywords (Original Language):
Author Name | University of Author | Faculty of Author |
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Abstract (2. Language):
Granulocytic sarcoma is a rare extramedullary tumor that originates from the primitive granulocytic cells. Granulocytic
sarcoma develops during the courses of acute myleoid leukemia, myelodisplastic syndrome and myeloproliferative
diseases and frequently it is observed on the bones, soft tissue, periost, lymph nodes and skin. Here we
report a 60 year old female patient who is at first diagnosed as diffuse large B cell lymphoma according to the biopsy
result of the 6x10 cm nodular lesion on the anterolateral side of her left calf and at last diagnosed as granulocytic
sarcoma upon reevaluation of the biopsy material. Granulocytic sarcomas are frequently confused with
lymphomas or the sarcomas. Here the difficulties of the diagnosis of granulocytic sarcoma is discussed and reviewed
in association with the literature.
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Abstract (Original Language):
Granülositik sarkom; primitif granülositik hücrelerden köken alan, nadir görülen, ekstramedüller bir tümördür. Granülositik
sarkom; akut myeloid lösemiler, myelodisplastik sendrom ve myeloproliferatif hastal›klar›n seyrinde geliflir
ve s›kl›kla kemik, yumuflak doku, periost, lenf nodlar› ve deride görülür. Biz burada, sol bald›r ön-yan yüzde
lokalize, 6x10 cm. boyutlar›nda, nodüler görünümlü, biyopsi incelemesinde önce diffüz büyük B hücreli lenfoma
tan›s› alan, ancak biyopsi materyalinin yeniden de¤erlendirilmesi socunda granülositik sarkom tan›s› konan 60-yafl›
nda bir kad›n hastay› bildiriyoruz. Granulositik sarkomlar tan› aflamas›nda s›k olarak lenfomalar veya sarkomlar
ile kar›flabilmektedir. Burada, granülositik sarkom tan›s› konulurken, karfl›lafl›lan güçlükler irdelendi ve literatür
eflli¤inde yeniden gözden geçirildi
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