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OSTEOGENEZİS İMPERFEKTA: BİR OLGU SUNUMU

OSTEOGENESIS IMPERFECTA: A CASE REPORT

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Abstract (2. Language): 
Osteogenesis imperfecta, or brittle bone disease, is a heritable disorder characterized by increased bone fraglitty. This article reports the case of a 7 year old child diagnosed with type I osteogenesis imperfecta, assessing the cinnical features observed, with emphasis on the histological, oral and dental findings. The histological examination of dentin often reveals presence of irregular dentinal tubules, amorphous areas and poor calcification. All caries teeth treated with stainless steel crowns. The extreme bone fraglitty seen in patients suffering from osteogenesis imperfecta pose a series of problems with regard to behavior management and rendernng of quaitty dental treatment.
Abstract (Original Language): 
Osteogenezis imperfekta veya krrigan kemik hastalığı, kemik kağanlığında artış ile karakterize kalttımsal brr bozukluktur. Bu olgu raporunda tip I tansı konan 7 yaşında brr çocuğun diş, ağız ve histolojik bulguları vurgulanmıştır ve kiinik özelikkleri değerlendirilmiştir. Dentinin histolojik incelenmesinde, zayıfkalsifiye olmuş, şekilsiz aaanaar ve düzensiz dentin tubulleri gözlemlenmiştir. Çürük dişler, paslanmaz çeiik kuronlar kullanılarak restore edilmiştir. Bu hastalar, şiddetli kemik kırı/ma/arından zarar gördüklerinden dolayı, nitelikli diş tedavilerini sağlamak ve davranış yönetimi hususunda bir dizi sorunlar üzerinde durmak gereklidir.
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